Cystic Fibrosis and Mental Health

FirstFrame John Hunter Hospital and John Hunter Children's Hospital Cystic Fibrosis services are part of a national research project to identify and respond to mental health concerns of people with Cystic Fibrosis. Clinical staff have commenced routine mental health screening of Cystic Fibrosis patients as a priority during clinical visits. The teams will need to build strong connections with local mental health care providers across the district for appropriate and efficient referral and support.
BMJ Best Practice logo logo Cystic fibrosis
HNELHD logo Policy compliance procedure. Cystic fibrosis management. PD2017_013:PCP 2
HNE Health Libraries logo Sheehan J, Hiscock H, Massie J, Jaffe A, Hay M. Caregiver coping, mental health and child problem behaviours in cystic fibrosis: a cross-sectional study. Int J Behav Med. 2014;21(2):211-20.
HNE Health Libraries logo Besier T, Goldbeck L. Growing up with cystic fibrosis: achievement, life satisfaction, and mental health. Qual Life Res. 2012;21(10):1829-35.

Cystic fibrosis 101    
FirstFrame Professor Peter Wark
Centre for Healthy Lungs, University of Newcastle
Department of Respiratory and Sleep Medicine, John Hunter Hospital
NHMRC Centre of Excellence in Severe Asthma
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Open access logo Eckford PD, Li C, Ramjeesingh M, Bear CE. Cystic fibrosis transmembrane conductance regulator (CFTR) potentiator VX-770 (ivacaftor) opens the defective channel gate of mutant CFTR in a phosphorylation-dependent but ATP-independent manner. J Biol Chem. 2012;287(44):36639-49.
Open access logo Ramsey BW, Davies J, McElvaney NG, Tullis E, Bell SC, Drevinek P, et al. A CFTR potentiator in patients with cystic fibrosis and the G551D mutation. N Engl J Med. 2011;365(18):1663-72.
Open access logo Wainwright CE, Elborn JS, Ramsey BW, Marigowda G, Huang X, Cipolli M, et al. Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR. N Engl J Med. 2015;373(3):220-31.
HNE Health Libraries logo Quittner AL, Goldbeck L, Abbott J, Duff A, Lambrecht P, Sole A, et al. Prevalence of depression and anxiety in patients with cystic fibrosis and parent caregivers: results of The International Depression Epidemiological Study across nine countries. Thorax. 2014;69(12):1090-7.

Cystic fibrosis 102    
FirstFrame Dr Jodi Hilton
Centre Director, Cystic Fibrosis Centre
Paediatric Respiratory Physician, John Hunter Children's Hospital
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The lived experience of cystic fibrosis    
FirstFrame Ms Ashlee Peck
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Caring for a child with cystic fibrosis    
FirstFrame Ms Wendy Wood Flash Screencast
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What am I going to do with my CF patient?    
FirstFrame Dr Ben Britton
Clinical and Health Psychologist
Consultant Liaison Psychiatry
Mater Hospital
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CIAP logo Ernst MM, Johnson MC, Stark LJ. Developmental and psychosocial issues in cystic fibrosis. Pediatr Clin North Am. 2011;58(4):865-85, x.